Snapshot
- A 2-day-old neonate presents with bilious vomiting and irritability. On physical examination, she has abdominal distention and high-pitched bowel sounds. Barium enema radiograph reveals a dilated sigmoid colon with a column of barium resembling a “coffee bean”.
Introduction
- Malrotation of gut from errors during development increases risk of volvulus
- Volvulus (typically, midgut)
- abnormal rotation of bowel
- strangulation of SMA
- compromised blood flow to bowel
- Epidemiology
- most common in newborns
- males > females
- Associated conditions
- situs inversus
- cardiovascular defects
- heterotaxy
- gastroschisis/omphalocele
Presentation
- Symptoms
- neonates
- bilious vomiting within first week of life
- colicky pain
- older patients
- bilious or nonbilious vomiting
- crampy abdominal pain
- change in bowel pattern
- nausea
- neonates
- Physical exam
- abdominal distention
- abdominal tenderness
Evaluation
- abdominal radiography
- may have air fluid levels
- upper GI imaging with barium enema
- “bird beak” appearance at site of rotation
- failure of duodenum to cross midline = malrotation
Differential Diagnosis
Treatment
- Malrotation without volvulus
- elective Ladd procedure
- Malrotation with volvulus (symptomatic or acute abdomen)
- emergent endoscopic decompression
- surgical decompression
Prognosis, Prevention, and Complications
- Prognosis
- good with treatment
- Complications
- bowel necrosis
- perforation
- sepsis